Exhale

The official blog of the Lung Institute.

End Stage Pulmonary Fibrosis Life Expectancy: What to Expect

End Stage Pulmonary Fibrosis Life Expectancy: What to Expect

Pulmonary Fibrosis (PF) is a disease characterized by the excessive build-up of scar tissue within the lungs, restricting breathing. And for those that live with it, they are well aware of the incremental stages of the disease’s progression. Although these stages are classified into terms such as mild, early, severe and advanced, it is the later stages of pulmonary fibrosis that can be of the most concern to those with the disease. As the disease progresses to the end stage, these effects can have a significant effect on disease symptoms and life expectancy. With that in mind, it’s best to be aware of one’s disease and how it progresses to gain a better understanding of what to expect and how best to prepare.

With your health in mind, the Lung Institute is here to give you the information you need on End Stage Pulmonary Fibrosis Life Expectancy: What to Expect and How to Prepare.

End Stage Pulmonary Fibrosis Life Expectancy: What Is It?

Let’s start with the basics: as we mentioned before, end stage pulmonary fibrosis staging is conducted using a patient’s forced vital capacity (FVC) score taken from a pulmonary function test. Where scores above 75% would equate to being mild PF, scores within the range of 25 to 49 (or less) are considered to be severe. Those within the severe to very severe category of pulmonary fibrosis staging are considered to be within end-stage pulmonary fibrosis.

As with any disease, PF disease progression is highly specific to the individual themselves, meaning that the decline in pulmonary health can occur rapidly for some or more slowly for others. This can mean the difference between a life with months left, or years, depending on one’s personal genetics and health-conscious habits (diet, exercise, abstention from smoking), but more on that later.

End Stage Pulmonary Fibrosis Life Expectancy: What to Expect

What Can I Expect? Signs & Symptoms

So you’ve been told you have end stage pulmonary fibrosis either by your pulmonary specialist or primary physician. What should you expect? The primary symptom of end stage pulmonary fibrosis is shortness of breath, a symptom that grows more acute as time goes on. As the diseases develops into this final stage, other commonly associated symptoms include:

  • Chest pain
  • Depression
  • Poor appetite
  • Increased anxiety
  • Bothersome cough
  • Becoming housebound
  • Reduced lung function
  • Disturbed sleep patterns
  • Need for intensive home support
  • Frequent flare-ups and hospitalizations
  • Increased severity in shortness of breath
  • Difficulty maintaining a healthy body weight

How Can I Prepare and Improve My Health?

Although end-stage pulmonary fibrosis is a difficult position to be in as it pertains to respiratory health, it is not the end. Various lifestyle changes to diet, weight, exercise, and smoking cessation can have a profound effect on the frequency and severity of flare-ups within those with advanced PF. To start, learn to eat healthier. Avoid fatty, salty, and spicy foods that could spark symptom flare-ups. Instead, focus on oxygen-rich food such as antioxidant fruits, smaller portions, and balanced meals of whole grains, non-cruciferous vegetables, and grilled protein.

In regards to weight and exercise, you can do a variety of healthy exercises from the comfort of your living room. Simply get the heart-rate moving to improve blood-oxygen flow–a standing squat should suffice. Lastly, quitting smoking is by far the best decision you can make for your respiratory health. This can be an extremely difficult proposition, but the time you will gain from giving up cigarettes will be well worth the sacrifice.

End Stage Pulmonary Fibrosis Life Expectancy: What to Expect

Moving Forward

End stage pulmonary fibrosis life expectancy is a topic that many would rather avoid, however, it’s vital to understanding one’s options as they navigate the management of their health. Though PF can seem impossible to overcome, changing one’s diet and consistently exercising are among the best lifestyle changes one can do aside from quitting smoking. When lifestyle changes fail to improve your quality of life in the way that you may expect, it may be time to consider cellular therapy. Rather than simply addressing the symptoms of lung disease, cellular therapy may directly affect disease progression and may improve quality of life and pulmonary function.

If you or a loved one suffers from a chronic disease like pulmonary fibrosis, COPD, ILD or other symptoms of lung disease, the Lung Institute may be able to help with a variety of adult cellular therapy options. Contact us today at (800) 729-3065 to see if you qualify for cellular therapy, and find out what cellular therapy could mean for you.

Interested in our article on End Stage Pulmonary Fibrosis Life Expectancy: What to Expect? Share your thoughts and comments below.

13 Comments

  1. Lung Institute

    6 months ago

    Jayne:

    We are able to treat patients at any stage of lung disease, though catching it earlier is obviously better. It is difficult to tell about how things will progress. It is all very much an individual basis. Our cellular treatments have improved the quality of life in many patients. People who could not walk to their mailbox are able to walk around the block or ride a bike.

    We’re happy to answer your questions about cellular therapy, so feel free to contact us at (855) 313-1149 to speak one-on-one with a patient coordinator. We look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  2. JAYNE

    6 months ago

    My faTHER WAS DIAGNOSED WITH SEVERE PULMONARY FIBROSIS YESTERDAY. HE IS 84. tHE SCARRING IS VERY NOTICEABLE ON THE XRAY. hIS DRY COUGH AND WEIGHT LOSS ADD TO THIS. AT THAT AGE WOULD YOU SAY THIS IS END STAGE? OF LATE HE HAS TAKEN TO HIS ROOM AND SAT WITH THE HEATER ON AS HE CAN’T GET WARM. WILL HE END UP WITH AN OXYGEN BOTTLE FOR AIR? CAN THIS BE REVERSED? hOW RAPID IS THE DECLINE WHEN YOU ARE ADVANCED IN YEARS? THANK YOU

  3. Lung Institute

    6 months ago

    Paul:

    Thank you for your comment and question. Mucus is a common problem for someone with a chronic lung disease. It is usually associated with a cough.

    Our team has a wealth of knowledge about cellular therapy, treatment, candidacy and cost. We’re happy to answer your questions. Feel free to give us a call at (855) 313-1149 to speak one-on-one with our dedicated medical team. We look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  4. paul g

    6 months ago

    I have IPF and a lot of mucus. I s mucus associated with pulmonary fibrosis. I see no mention of in in all your responses . Most times I have to create a vacuum within my mouth to get it our of my throat and cough a lot . Is this part of IPF?
    Thanks for your reply.

  5. Lung Institute

    7 months ago

    Shelley:

    Thank you for contacting us and we are very sorry to hear about your sister.

    It’s best to speak one-on-one with one of our well-qualified patient coordinators. They have a wealth of knowledge about cellular therapy, treatment options, candidacy and cost. Chronic lung diseases affect everyone differently, so we can best help you by speaking with you over the phone. Feel free to contact us at (855) 313-1149, and we look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  6. Shelley

    7 months ago

    When is it too late to try cell transplant? My sister is in an acute care hospital for her Pf. Its at the advanced stage because she needs 60% of hi flow oxygen. She cannot even take a step without increasing the oXygeN. She also needs dialysis so her doctors at Mass General told
    Her she was not qUalified for a lUng tranSplant because she would also need a new kidney.
    She is only 54 and we found out on Oct 4 she has PF. She has been in and out of the hospital since the end of july. Can anyone help?

  7. Lung Institute

    8 months ago

    Debbie:

    There is really no way to determine life expectancy with a lung disease because each case is different. Please take a look at these blog articles to provide you with information. For many of our patients, treatment has helped them feel better and breathe more easily.

    We’re happy to answer your questions about cellular therapy for lung disease. Our dedicated medical team has a wealth of knowledge about cellular therapy, treatment options, candidacy and more. So, feel free to contact us at (855) 313-1149 to speak one-on-one with someone from our medical team over our secure phone line. We look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  8. Lung Institute

    8 months ago

    Mandar:

    We would suggest you continue to see your primary doctor and follow what ever treatment plans are recommended. If you do want to explore cell therapy for lung disease, you can learn more about cellular treatments and have your questions answered by one of our qualified patient coordinators. Feel free to contact us at (855) 313-1149 for more information. We look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  9. Debbie

    9 months ago

    I have mild pulumonary fibrosis, how long have I got to live …….”I also have COPd.

  10. Phoebe

    11 months ago

    Hi,

    Idiopathic pulmonary fibrosis affects everyone differently and at varying rates of progression. We recommend discussing your questions and concerns about a tracheostomy with your doctor. Because your doctor knows you and your health situation well, he or she will be able to best guide you, answer your questions and discuss your concerns.

    Kind Regards,

    The Lung Institute

  11. Unknown

    11 months ago

    What do you think of putting in a tracheostomy to a person with IPF

  12. Phoebe

    1 year ago

    Dear Alice,

    First and foremost, we’re sorry to hear that Mike has passed away. IPF, pneumonia and the conditions that come along with having chronic lung diseases are very challenging. Again, we send our deepest sympathies to you and your family during this difficult time.

    Kind Regards,

    The Lung Institute

  13. Alice Fonda Henson Workman

    1 year ago

    My husband had cell replacement therapy soon as he was diagnosed with IPF. As far as we could tell, it did nothing. However, the Lung Institute was very frank about stating up front that it might not help at all. The incessant coughing and struggle for breath was nerve wracking for all of us.

    His father died from some sort of lung problem. We were told pneumonia, but my mother had mentioned that something was wrong with Dr. Workman months before hand. We were living in MT at the time and Mike’s parents were in Picayune. When he was hospitalized in Feb. 1997, Mike was unable to get a plane ticket to be there before he died. I have often wondered if his condition was not more than pneumonia. Dr. Workman was a navy doctor who specialized in hyperbaric medicine and had made many dives.

    We are grateful to the Lung Institute and Genentech (sp?) for the help and support they gave us during this process. Mike lost his battle in the early hours of Feb. 14.

All claims made regarding the efficacy of Lung Institute's treatments as they pertain to pulmonary conditions are based solely on anecdotal support collected by Lung Institute. Individual conditions, treatment and outcomes may vary and are not necessarily indicative of future results. Testimonial participation is voluntary. Lung Institute does not pay for or script patient testimonials.

As required by Texas state law, the Lung Institute Dallas Clinic has received Institutional Review Board (IRB) approval from MaGil IRB, now Chesapeake IRB, which is fully accredited by the Association for the Accreditation of Human Research Protection Program (AAHRPP), for research protocols and procedures. The Lung Institute has implemented these IRB approved standards at all of its clinics nationwide. Approval indicates that we follow rigorous standards for ethics, quality, and protections for human research.