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What are the Final Stages of Pulmonary Fibrosis?

What are the Final Stages of Pulmonary Fibrosis?

Pulmonary fibrosis is a type of chronic lung disease that occurs when lung tissue becomes scarred or damaged. The stiff, thickened tissue obstructs the free passage of oxygen into the bloodstream through the walls of the lungs’ tiny air sacs (alveoli). Because pulmonary fibrosis is a progressive disease, it will worsen over time. If you’re living with pulmonary fibrosis, you might be wondering what are the final stages of pulmonary fibrosis?

What causes pulmonary fibrosis?

While there are many possible causes of pulmonary fibrosis, such as occupational and environmental factors, autoimmune disorders, infections, genetics and reaction to medications, many times the cause of pulmonary fibrosis is unknown. When the cause of the disease cannot be identified, pulmonary fibrosis of no known cause is called idiopathic pulmonary fibrosis.

What are the symptoms of pulmonary fibrosis?

For some people, their symptoms progress quickly while others remain mild to moderate for years. People may also experience episodes of symptom flare-ups. Eventually, people with pulmonary fibrosis will experience worsening symptoms, which is often a sign of rapid disease progression. The most common symptom is feeling increasingly out of breath.

Pulmonary Fibrosis Symptoms:

  • Fatigue
  • Coughing
  • Weakness
  • Achy Joints
  • Weight Loss
  • Shortness of Breath

What are the final stages of pulmonary fibrosis?

What are the Final Stages of Pulmonary Fibrosis?

Whether you have pulmonary fibrosis or serve as a caregiver to someone with the disease, knowing the signs of the final stages of pulmonary fibrosis makes you more prepared and better informed. Pulmonary fibrosis is a progressive disease; in other words, it steadily worsens over time. People in the end-stages of progressive lung disease will experience a gradual worsening of their ability breathe. The nature of the progression of the disease is that after each flare-up, lung function is degraded and does not return to the level it was before the flare-up.

As the disease progresses, the lungs become less efficient. Simple tasks, even as simple as talking or eating, can make someone with pulmonary fibrosis feel out of breath and fatigued. Having enough oxygen is essential to a properly functioning body. As lung function declines, low blood oxygen levels cause other issues.

If you or your loved one is distressed at having entered the final stages of pulmonary fibrosis, it’s important to share these feelings with your doctor. Your doctor has resources to help you and your loved one cope with the progression of this challenging disease.

What are the treatment options for people with pulmonary fibrosis?

While pulmonary fibrosis is not curable, it is treatable. Many doctors may prescribe a combination of corticosteroids, medications that suppress the immune system, inhalers, oxygen therapy, nutritional counseling, lung transplant surgery and pulmonary rehabilitation.

Some patients have found alternative treatments, such as stem cell therapy, helpful in treating pulmonary fibrosis and improving their quality of life. Stem cell treatment at the Lung Institute uses stem cells derived from the patient’s body, known as autologous stem cells. After Lung Institute physicians extract stem cells from a patient’s blood or bone marrow tissue, the cells are separated and returned to the patient intravenously. Once returned, stem cells flow through the heart and into the lungs, where they aggregate and can promote the healing of lung tissue. You can learn more about this process by reading Lung Institute reviews and patients’ results, or by watching the patients themselves tell you about their experiences in patient testimonials.

We hope we’ve answered the question “what are the final stages of pulmonary fibrosis” well, and that you’ve found some answers to your questions. We understand how challenging this condition can be, and we’re here to help. If you or a loved one has pulmonary fibrosis, or another chronic lung disease, and would like more information about stem cell treatment options at the Lung Institute, please contact us at (800) 729-3065.


  1. Lung Institute

    3 months ago


    We are very sorry to hear about your husband’s condition. We would recommend calling one of our patient coordinators and discussing your husband’s situation.

    We’re happy to talk with you one-on-one about your questions and concerns regarding stem cell treatment, candidacy and cost, so feel free to contact us at (855) 313-1149. We look forward to hearing from you soon.


    The Lung Institute

  2. Dolores Davis

    5 months ago

    My husband has been DIAGNOSED with pulmonary fiberosis. he has been told my his dr. willers from st. thomas hospital at nashville that he is in the end stage. i want to know what to expect.she said his lung funciton is 38%. what do i watch for?

  3. Phoebe

    5 months ago

    Dear Christopher,

    First and foremost, we’re sorry to hear about the challenges your father has been facing with idiopathic pulmonary fibrosis (IPF). Like your father, many people with IPF have difficulty with tasks like walking from room to room. IPF, even during end-stage, affects everyone differently and at varying rates of progression. It’s hard to know how long the process may take, and it’s impossible to estimate life expectancy. Your father’s doctor knows him and his health situation well, so his doctor will be able to best guide you regarding your father’s IPF. It’s completely normal for people with IPF to feel depressed and anxious. If your father is having trouble with depression or anxiety, we recommend seeking the guidance of your father’s doctor about seeing a trained mental health professional. Your father’s doctor will likely have recommendations for therapists and counselors who help people living with chronic illnesses and their families. Your father is very fortunate to have you to support him through this challenging time.

    Kind Regards,

    The Lung Institute

  4. Christopher B

    5 months ago

    note: apologize for using all caps. I’m not yelling : )….my caps lock is off so not sure what this is occurring.


    my father is 73 and diagnosed in January will idiopathic pulmonary fibrosis. he is currently on 8.5L of constant oxygen and is housebound with limited mobility. his oxygen level drops with any activity performed. he is now using his wheel chair to go from room to room to conserve energy. he is on hospice care and received morphine periodically to help control the sensation of breathing depravation. he was evaluated for a lung transplant at st. joseph’s hospital in phoenix but denied the transplant. he was concerned with quality of life so was at peace with their decision not to offer him a transplant.

    my question is how long this end stage process could take. he is a positive person but mentally this is becoming challenging for him. his demand for oxygen regularly increases and we now have two concentrators so that he can receive more than 10L (maximum of individual machines). I hate seeing his suffering.

  5. Phoebe

    6 months ago

    Hi Linda,

    There isn’t an age limit for stem cell therapy. At the Lung Institute, we’ve treated people in their forties and people in their eighties and nineties. We’re happy to answer your questions about stem cell therapy for people with IPF, so feel free to contact us at (855) 313-1149. We look forward to hearing from you soon.

    Best Regards,

    The Lung Institute

  6. Linda

    6 months ago


  7. Phoebe

    7 months ago

    Dear Donna,

    First and foremost, we’re sorry to hear about the challenges you have been facing with IPF. It’s important to talk with your doctor about any changes you are noticing with your symptoms or overall health. You and your doctor can work together to develop the best IPF treatment plan for you. We’re happy to answer your questions about stem cell treatment for IPF, so feel free to contact us at (855) 313-1149.

    Best Regards,

    The Lung Institute

  8. Donna Dickerson

    7 months ago

    Ive been Diagnosed with ipf lung disease 4 months ago , i dont know what stage im in , all i know is that my QUALITY of lIfe has slowed dOwn .my energy level has DROPPED & i Cough all the time & theres pain in my right lung .

  9. PB

    1 year ago

    Dear Will,

    Thank you for your comment. The Lung Institute performs adult stem cell therapy, which uses stem cells derived from the patient’s own body. We don’t perform lung transplants. If you’re interested in learning more about stem cell treatment options, feel free to contact us at (855) 313-1149. Our patient coordinators have a wealth of knowledge about stem cells, treatment, cost and candidacy, and they are happy to answer your questions. We look forward to hearing from you soon.

    Best Regards,

    The Lung Institute

  10. Will Adams

    1 year ago

    I’m familiar with BMAC use in orthopedic and spine surgeries. I have a relative being tested for a lung transplant due to IPF. Are there any benefits for using BMAC in a lung transplant, and if so, how would it be used?

  11. PB

    1 year ago

    Dear Clinton,

    First and foremost, we’re sorry to hear about the challenges you have been facing with pulmonary fibrosis. Many people with chronic lung diseases find cleaning their home difficult. Many of our patients have seen positive results after receiving treatment. You can watch their stories by clicking here. We’re happy to answer any questions you have regarding stem cell treatment options, so feel free to contact us today at (855) 313-1149 to speak one-on-one with a patient coordinator. We look forward to hearing from you soon.

    Kind Regards,

    The Lung Insititute

  12. Clinton Deiters

    1 year ago

    I’m Final Stage going thru this over 6 tears I mean years or both, It takes me all day to clean my one bedroom home a little at a time. Help Me!

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* All treatments performed at Lung Institute utilize autologous stem cells, meaning those derived from a patient's own body. No fetal or embryonic stem cells are utilized in Lung Institute's procedures. Lung Institute aims to improve patients' quality of life and help them breathe easier through the use of autologous stem cell therapy. To learn more about how stem cells work for lung disease, click here.

All claims made regarding the efficacy of Lung Institute's treatments as they pertain to pulmonary conditions are based solely on anecdotal support collected by Lung Institute. Individual conditions, treatment and outcomes may vary and are not necessarily indicative of future results. Testimonial participation is voluntary. Lung Institute does not pay for or script patient testimonials.

Under current FDA guidelines and regulations 1271.10 and 1271.15, the Lung Institute complies with all necessary requirements for operation. The Lung Institute is firmly in accordance with the conditions set by the FDA for exemption status and conducts itself in full accordance with current guidelines. Any individual who accesses Lung Institute's website for information is encouraged to speak with his or her primary physician for treatment suggestions and conclusive evidence. All information on this site should be used for educational and informational use only.

As required by Texas state law, the Lung Institute Dallas Clinic has received Institutional Review Board (IRB) approval from MaGil IRB, now Chesapeake IRB, which is fully accredited by the Association for the Accreditation of Human Research Protection Program (AAHRPP), for research protocols and stem cell procedures. The Lung Institute has implemented these IRB approved standards at all of its clinics nationwide. Approval indicates that we follow rigorous standards for ethics, quality, and protections for human research.