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What are the Final Stages of Pulmonary Fibrosis?

What are the Final Stages of Pulmonary Fibrosis?

Pulmonary fibrosis is a type of chronic lung disease that occurs when lung tissue becomes scarred or damaged. The stiff, thickened tissue obstructs the free passage of oxygen into the bloodstream through the walls of the lungs’ tiny air sacs (alveoli). Because pulmonary fibrosis is a progressive disease, it will worsen over time. If you’re living with pulmonary fibrosis, you might be wondering what are the final stages of pulmonary fibrosis?

What causes pulmonary fibrosis?

While there are many possible causes of pulmonary fibrosis, such as occupational and environmental factors, autoimmune disorders, infections, genetics and reaction to medications, many times the cause of pulmonary fibrosis is unknown. When the cause of the disease cannot be identified, pulmonary fibrosis of no known cause is called idiopathic pulmonary fibrosis.

What are the symptoms of pulmonary fibrosis?

For some people, their symptoms progress quickly while others remain mild to moderate for years. People may also experience episodes of symptom flare-ups. Eventually, people with pulmonary fibrosis will experience worsening symptoms, which is often a sign of rapid disease progression. The most common symptom is feeling increasingly out of breath.

Pulmonary Fibrosis Symptoms:

  • Fatigue
  • Coughing
  • Weakness
  • Achy Joints
  • Weight Loss
  • Shortness of Breath

What are the final stages of pulmonary fibrosis?

What are the Final Stages of Pulmonary Fibrosis?

Whether you have pulmonary fibrosis or serve as a caregiver to someone with the disease, knowing the signs of the final stages of pulmonary fibrosis makes you more prepared and better informed. Pulmonary fibrosis is a progressive disease; in other words, it steadily worsens over time. People in the end-stages of progressive lung disease will experience a gradual worsening of their ability breathe. The nature of the progression of the disease is that after each flare-up, lung function is degraded and does not return to the level it was before the flare-up.

As the disease progresses, the lungs become less efficient. Simple tasks, even as simple as talking or eating, can make someone with pulmonary fibrosis feel out of breath and fatigued. Having enough oxygen is essential to a properly functioning body. As lung function declines, low blood oxygen levels cause other issues.

If you or your loved one is distressed at having entered the final stages of pulmonary fibrosis, it’s important to share these feelings with your doctor. Your doctor has resources to help you and your loved one cope with the progression of this challenging disease.

What are the treatment options for people with pulmonary fibrosis?

While pulmonary fibrosis is not curable, it is treatable. Many doctors may prescribe a combination of corticosteroids, medications that suppress the immune system, inhalers, oxygen therapy, nutritional counseling, lung transplant surgery and pulmonary rehabilitation.

Some patients have found alternative treatments, such as cellular therapy, helpful in treating pulmonary fibrosis and improving their quality of life. Cellular treatment at the Lung Institute uses cells derived from the patient’s body. After Lung Institute physicians extract cells from a patient’s blood, the cells are separated and returned to the patient intravenously. Once returned, cells flow through the heart and into the lungs, where they aggregate and can promote the healing of lung tissue. You can learn more about this process by reading Lung Institute reviews and patients’ results, or by watching the patients themselves tell you about their experiences in patient testimonials.

We hope we’ve answered the question “what are the final stages of pulmonary fibrosis” well, and that you’ve found some answers to your questions. We understand how challenging this condition can be, and we’re here to help. If you or a loved one has pulmonary fibrosis, or another chronic lung disease, and would like more information about cellular therapy options at the Lung Institute, please contact us at (800) 729-3065.

18 Comments

  1. Lung Institute

    4 months ago

    Imran:

    Thank you for your comment and question. We are sorry to hear about your father’s condition.

    We have treated patients at all stages of lung disease and gotten results, though the earlier the better.

    We’re happy to answer your questions about cellular therapy for chronic lung diseases. We have a dedicated medical team who have a wealth of knowledge about cellular therapy, treatment options, candidacy, cost and more. So, feel free to give us a call at (855) 313-1149. We look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  2. imran

    4 months ago

    My father has ben DIAGNOSED IPF. Now he is on oxygen 24/7 and lying on bed. little movement drops his oxygen. his oxygen intake is 2litres. his age is 75. he has been prescribed perfrindon. can cell therapy improve his condition.

  3. Lung Institute

    5 months ago

    Irene:

    We are sorry to hear about your husband’s condition and hope for the best. Unfortunately, your doctor or specialist is probably most knowledgeable to treat your husband.

    If you are interested in pursuing our cellular treatments, our dedicated medical team has a wealth of knowledge about cellular therapy, treatment options, candidacy, cost and more. We’re happy to answer your questions, so feel free to give us a call at (855) 313-1149. We look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  4. irene

    5 months ago

    my husband is in his 10th year of Ipf. we feel blessed that he ha endured this long with somewhat minimum bad side effects. He is on oxygen (has been for 10 months now) and is taking a drug called ESPIRIT which seemed to have slowed down the progression of the fibrosis. However, he is down to 110 lbs, has no energy, no appetite and is dealing with depression. and at times muscle spasms. He spends most of his days lying around on the couch or in bed. One of our concerns right now is that he is having bad hot spells and/ or severe chills often. We have had no definite answer for this symptom from his doctor. when it happens he gets real upset. my husband has always been a very active person,so it is very hard for him to deal with this disease. what can you tell me about these symptoms and what can i do to alleviate them/

  5. Lung Institute

    6 months ago

    Brenda:

    We are sorry to hear about your mother’s condition. Our first suggestion would be to see her primary doctor or specialist and see what they recommend. We are assuming your mother has a lung disease. If she does have a lung disease, then our cellular treatments may provide help.

    You can learn more about cellular treatment options and have your questions answered by one of our patient coordinators. Feel free to contact us at (855) 313-1149 for more information. We look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  6. Brenda

    6 months ago

    I live with my mom she is 80 and has this horrible disease from radiation when she had breast cancer 12 yrs ago it is painful watching her go thru this she suppose to wear her oxygen 24/7 she only wears it when her oxygen drops and cough worsens what you suggest

  7. Lung Institute

    9 months ago

    Dolores:

    We are very sorry to hear about your husband’s condition. We would recommend calling one of our patient coordinators and discussing your husband’s situation.

    We’re happy to talk with you one-on-one about your questions and concerns regarding cellular treatment, candidacy and cost, so feel free to contact us at (855) 313-1149. We look forward to hearing from you soon.

    Sincerely,

    The Lung Institute

  8. Dolores Davis

    11 months ago

    My husband has been DIAGNOSED with pulmonary fiberosis. he has been told my his dr. willers from st. thomas hospital at nashville that he is in the end stage. i want to know what to expect.she said his lung funciton is 38%. what do i watch for?

  9. Phoebe

    12 months ago

    Dear Christopher,

    First and foremost, we’re sorry to hear about the challenges your father has been facing with idiopathic pulmonary fibrosis (IPF). Like your father, many people with IPF have difficulty with tasks like walking from room to room. IPF, even during end-stage, affects everyone differently and at varying rates of progression. It’s hard to know how long the process may take, and it’s impossible to estimate life expectancy. Your father’s doctor knows him and his health situation well, so his doctor will be able to best guide you regarding your father’s IPF. It’s completely normal for people with IPF to feel depressed and anxious. If your father is having trouble with depression or anxiety, we recommend seeking the guidance of your father’s doctor about seeing a trained mental health professional. Your father’s doctor will likely have recommendations for therapists and counselors who help people living with chronic illnesses and their families. Your father is very fortunate to have you to support him through this challenging time.

    Kind Regards,

    The Lung Institute

  10. Christopher B

    12 months ago

    note: apologize for using all caps. I’m not yelling : )….my caps lock is off so not sure what this is occurring.

    morning

    my father is 73 and diagnosed in January will idiopathic pulmonary fibrosis. he is currently on 8.5L of constant oxygen and is housebound with limited mobility. his oxygen level drops with any activity performed. he is now using his wheel chair to go from room to room to conserve energy. he is on hospice care and received morphine periodically to help control the sensation of breathing depravation. he was evaluated for a lung transplant at st. joseph’s hospital in phoenix but denied the transplant. he was concerned with quality of life so was at peace with their decision not to offer him a transplant.

    my question is how long this end stage process could take. he is a positive person but mentally this is becoming challenging for him. his demand for oxygen regularly increases and we now have two concentrators so that he can receive more than 10L (maximum of individual machines). I hate seeing his suffering.

  11. Phoebe

    1 year ago

    Hi Linda,

    There isn’t an age limit for cell therapy. At the Lung Institute, we’ve treated people in their forties and people in their eighties and nineties. We’re happy to answer your questions about cellular therapy for people with IPF, so feel free to contact us at (855) 313-1149. We look forward to hearing from you soon.

    Best Regards,

    The Lung Institute

  12. Linda

    1 year ago

    Can YOU TELL ME IF AT THE AGE OF 70 WOULD STEM CELL HELP ipf? mY HUSBAND HAS ipf AND HAS HAD IT FOR SEVERAL YEARS AND IS STARTING TO GET WORSE.

  13. Phoebe

    1 year ago

    Dear Donna,

    First and foremost, we’re sorry to hear about the challenges you have been facing with IPF. It’s important to talk with your doctor about any changes you are noticing with your symptoms or overall health. You and your doctor can work together to develop the best IPF treatment plan for you. We’re happy to answer your questions about cellular treatment for IPF, so feel free to contact us at (855) 313-1149.

    Best Regards,

    The Lung Institute

  14. Donna Dickerson

    1 year ago

    Ive been Diagnosed with ipf lung disease 4 months ago , i dont know what stage im in , all i know is that my QUALITY of lIfe has slowed dOwn .my energy level has DROPPED & i Cough all the time & theres pain in my right lung .

  15. PB

    2 years ago

    Dear Will,

    Thank you for your comment. The Lung Institute performs adult cell therapy, which uses cells derived from the patient’s own body. We don’t perform lung transplants. If you’re interested in learning more about cellular treatment options, feel free to contact us at (855) 313-1149. Our patient coordinators have a wealth of knowledge about cellular therapy, treatment, cost and candidacy, and they are happy to answer your questions. We look forward to hearing from you soon.

    Best Regards,

    The Lung Institute

  16. Will Adams

    2 years ago

    I’m familiar with BMAC use in orthopedic and spine surgeries. I have a relative being tested for a lung transplant due to IPF. Are there any benefits for using BMAC in a lung transplant, and if so, how would it be used?

  17. PB

    2 years ago

    Dear Clinton,

    First and foremost, we’re sorry to hear about the challenges you have been facing with pulmonary fibrosis. Many people with chronic lung diseases find cleaning their home difficult. Many of our patients have seen positive results after receiving treatment. You can watch their stories by clicking here. We’re happy to answer any questions you have regarding cellular treatment options, so feel free to contact us today at (855) 313-1149 to speak one-on-one with a patient coordinator. We look forward to hearing from you soon.

    Kind Regards,

    The Lung Insititute

  18. Clinton Deiters

    2 years ago

    I’m Final Stage going thru this over 6 tears I mean years or both, It takes me all day to clean my one bedroom home a little at a time. Help Me!

* Every patient is given a Patient Satisfaction Survey shortly after treatment. Responses to the 11-question survey are aggregated to determine patient satisfaction with the delivery of treatment.

^ Quality of Life Survey data measured the patient’s self-assessed quality of life and measurable quality of improvement at three months.

All claims made regarding the efficacy of Lung Institute's treatments as they pertain to pulmonary conditions are based solely on anecdotal support collected by Lung Institute. Individual conditions, treatment and outcomes may vary and are not necessarily indicative of future results. Testimonial participation is voluntary. Lung Institute does not pay for or script patient testimonials.

As required by Texas state law, the Lung Institute Dallas Clinic has received Institutional Review Board (IRB) approval from MaGil IRB, now Chesapeake IRB, which is fully accredited by the Association for the Accreditation of Human Research Protection Program (AAHRPP), for research protocols and procedures. The Lung Institute has implemented these IRB approved standards at all of its clinics nationwide. Approval indicates that we follow rigorous standards for ethics, quality, and protections for human research.

Each patient is different. Results may vary.