The official blog of the Lung Institute.
There are two major classifications for chronic lung diseases. One group of chronic lung diseases is classified as obstructive lung disease, which includes chronic obstructive pulmonary disease, (COPD) and emphysema. The other group is classified as restrictive lung disease. Examples of restrictive lung diseases include interstitial lung disease and pulmonary fibrosis. Understanding your condition is the first step to a better quality of life, and we’re here to help. Here are the facts you need to know about restrictive lung disease.
What is restrictive lung disease?
People with restrictive lung disease cannot fully fill their lungs with air because their lungs are restricted from fully expanding. People find it difficult to take a full breath. Often, restrictive lung disease results from a condition causing stiffness in the lungs themselves. Restrictive lung diseases are categorized as intrinsic and extrinsic.
Certain types of restrictive lung disease are called intrinsic restrictive lung disorders. Intrinsic disorders come from a problem within the lungs themselves.
Intrinsic Restrictive Lung Disorders include:
- Interstitial lung disease
- Idiopathic pulmonary fibrosis
- Pulmonary Fibrosis
Sometimes, restriction is caused by weak muscles, stiffness in the chest wall or damaged nerves. Extrinsic restrictive lung disorders cause lung problems to occur from disorders outside of the lungs. This means that the restriction and lung problems originate from outside of the lungs.
Extrinsic Restrictive Lung Disorders include:
- Pleural Effusion
- Myasthenia gravis
- Neuromuscular disease, such as muscular dystrophy or Lou Gehrig’s Disease (ALS)
Restrictive lung disease is characterized by reduced total lung capacity (TLC). Total lung capacity represents the amount of air present in the lungs after taking the deepest breath possible. TLC is determined during a pulmonary function test. Knowing the total lung capacity of someone with restrictive lung disease is important to confirm lung restriction and to measure the degree of restriction.
What are the restrictive lung disease symptoms?
There are several common symptoms with shortness of breath at the top of the list. In the early stages of the disease, shortness of breath may occur only with exertion. However, as the disease progresses, shortness of breath or breathlessness may occur with minimal activity or during rest.
Another common symptom is a chronic cough. Typically, the cough is dry, but it may also produce white sputum. Weight loss and fatigue are common symptoms as well. Many people find it challenging maintain a healthy weight and to have enough energy.
Some people with restrictive lung disease experience symptoms of depression and anxiety. These symptoms happen more often when the lung disease causes significant limitations.
What are the restrictive lung disease treatments?
Many types of restrictive lung diseases are progressive, meaning they will worsen over time. However, treatments are available and vary depending on the patient’s individual needs.
For example, Esbriet and Ofev are two FDA-approved medications sometimes used to treat idiopathic pulmonary fibrosis. Pulmonary fibrosis is a type of restrictive lung disease. Other types of treatments work to reduce inflammation and suppress the immune system. These medications include corticosteroids, azathioprine, cyclophosamide and methotrexate.
Many people with restrictive lung disease use oxygen therapy to help maintain blood oxygen levels. Sometimes, lung transplantation surgery is recommended in cases of severe or end-stage restrictive lung disease.
For people with certain types of restrictive lung disease, such as pulmonary fibrosis, interstitial lung disease, idiopathic pulmonary fibrosis or pneumoconiosis, cellular therapy is available. Cellular therapy works to promote healing from within the lungs, potentially improving lung function and quality of life.
Under the supervision of their doctors, some people have reduced their oxygen therapy use after treatment. If you or a loved one has pulmonary fibrosis, interstitial lung disease, pneumoconiosis or another chronic lung disease and would like to learn more about cellular therapy options, contact us at (800) 729-3065.